Mitochondrial chaperone BCS1
RBH JGI v2.0
RBH JGI v1.0
BDIQ01000006.1 : 112641 - 113240
"Protein translocase and chaperone required for Complex III assembly; member of the AAA ATPase family; forms a homo-oligomeric complex in the mitochondrial inner membrane that translocates the C-terminal domain of Rip1p from the matrix across the inner membrane, and then delivers it to an assembly intermediate of respiratory Complex III in an ATP-dependent reaction; also required for assembly of the Qcr10p subunit; mutations in human homolog BCS1L linked to neonatal diseases"
"Has domain(s) with predicted ATP binding, nucleoside-triphosphatase activity, nucleotide binding activity and role in mitochondrial respiratory chain complex III assembly"